Copyright
©The Author(s) 2025. Published by Baishideng Publishing Group Inc. All rights reserved.
World J Clin Cases. Oct 26, 2025; 13(30): 111020
Published online Oct 26, 2025. doi: 10.12998/wjcc.v13.i30.111020
Published online Oct 26, 2025. doi: 10.12998/wjcc.v13.i30.111020
Recurrent dermatofibrosarcoma protuberans involving the lacrimal sac: A case report
Bijnya Birajita Panda, Utkarsh Agarwal, Thilakraj Koppalu Lingaraju, Department of Ophtha
Sudhakar Gunasekar, Department of Surgical Oncology, Jawaharlal Institute of Postgraduate Medical Education & Research, Tamil Nadu 110029, India
Amit Kumar Adhya, Department of Pathology, All India Institute of Medical Sciences, Bhu
Author contributions: Panda BB designed and conducted the study; Panda BB and Koppalu Lingaraju T wrote the manuscript; Agarwal U provided clinical input; Panda BB and Gunasekar S critically analyzed the manuscript and provided crucial input that was essential for preparing the final version of the manuscript; Agarwal U and Koppalu Lingaraju T acquired the clinical data, prepared the first draft of the manuscript, searched the literature, and were responsible for the preparation of figures; Adhya AK provided histopathological data and figure preparation and critically analyzed the manuscript.
Informed consent statement: Informed written consent was obtained from the patient for publication of this report and any accompanying images.
Conflict-of-interest statement: The authors have no conflicts of interest to declare.
CARE Checklist (2016) statement: The authors have read the CARE Checklist (2016), and the manuscript was prepared and revised according to the CARE Checklist (2016).
Open Access: This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: https://creativecommons.org/Licenses/by-nc/4.0/
Corresponding author: Bijnya Birajita Panda, Assistant Professor, Department of Ophtha
Received: June 24, 2025
Revised: July 18, 2025
Accepted: August 13, 2025
Published online: October 26, 2025
Processing time: 112 Days and 22.6 Hours
Revised: July 18, 2025
Accepted: August 13, 2025
Published online: October 26, 2025
Processing time: 112 Days and 22.6 Hours
Core Tip
Core Tip: Periocular dermatofibrosarcoma protuberans (DFSP) of the lacrimal sac is extremely rare, often mimicking benign or inflammatory lesions, leading to delayed diagnosis. High clinical suspicion is warranted for slowly enlarging, firm, painless medial canthal masses. Histopathology with cluster of differentiation 34 immunopositivity confirms the diagnosis. Complete surgical excision with histologically clear margins is crucial to prevent recurrence, with consideration for Mohs micrographic surgery in select cases. Long-term follow-up is essential due to the locally aggressive nature of DFSP and potential for late recurrence. Early recognition and meticulous margin control are key to optimal functional and cosmetic outcomes.