Published online Nov 6, 2024. doi: 10.12998/wjcc.v12.i31.6500
Revised: August 9, 2024
Accepted: August 16, 2024
Published online: November 6, 2024
Processing time: 124 Days and 17.9 Hours
Miller fisher syndrome (MFS) is a variant of Guillain-Barré syndrome, an acute immune-mediated peripheral neuropathy that is often secondary to viral infections. Anti-ganglioside antibodies play crucial roles in the development of MFS. The positive rate of ganglioside antibodies is exceptionally high in MFS patients, particularly for anti-GQ1b antibodies. However, the presence of other ganglioside antibodies does not exclude MFS.
We present a 56-year-old female patient who suddenly developed right blepharoptosis and progressively worsening vision in both eyes. There were flu symptoms prior to onset, and a coronavirus disease 2019 test was positive. On physical examination, the patient exhibited bilateral extraocular muscle paralysis, weakened reflexes in both limbs, and impaired coordination. The cerebrospinal fluid examination results showed no obvious abnormalities. Bilateral peroneal nerve F-waves were not extracted. Serum anti-GD1b IgG and anti-GT1a IgG antibodies were positive. The patient received intravenous methylprednisolone (1000 mg/day), with the dosage gradually decreased. Additionally, intravenous high-dose immunoglobulin treatment was administered for 5 days (0.4 g/kg/day) from day 2 to day 6 of hospitalization. The patient’s symptoms improved after treatment with immunoglobulins and hormones.
Positive ganglioside antibodies may be used as supporting evidence for the diagnosis; however, the diagnosis of MFS is more reliant on clinical symptoms.
Core Tip: This case study reports a unique presentation of Miller fisher syndrome with positive anti-GQ1b and anti-GT1a antibodies alongside multiple autoimmune markers. While ganglioside antibodies offer supportive evidence, Miller fisher syndrome diagnosis primarily relies on clinical manifestations, emphasizing the importance of comprehensive clinical assessment in diagnosing this immune-mediated neuropathy.