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Case Report
©The Author(s) 2016. Published by Baishideng Publishing Group Inc. All rights reserved.
World J Clinical Cases. Sep 16, 2016; 4(9): 306-309
Published online Sep 16, 2016. doi: 10.12998/wjcc.v4.i9.306
Huge peripheral primitive neuroectodermal tumor of the small bowel mesentery at nonage: A case report and review of the literature
Zhe Liu, Yuan-Hong Xu, Chun-Lin Ge, Jin Long, Rui-Xia Du, Ke-Jian Guo
Zhe Liu, Yuan-Hong Xu, Chun-Lin Ge, Jin Long, Ke-Jian Guo, Department of Pancreatic Surgery, the First Hospital of China Medical University, Shenyang 110001, Liaoning Province, China
Rui-Xia Du, Department of Otorhinolaryngology, Fengtian Hospital, Shenyang Medical University, Shenyang 110001, Liaoning Province, China
Author contributions: All authors contributed to the acquisition of data, writing and revision of the manuscript.
Institutional review board statement: This case report is retrospective and was not antecedently reviewed by the Local Ethics committee of China Medical University.
Informed consent statement: The patient involved in this study gave his written informed consent authorizing use and disclosure of his protected health information.
Conflict-of-interest statement: The authors declared that they have no conflicts of interest to this work.
Correspondence to: Zhe Liu, MD, Department of Pancreatic Surgery, the First Hospital of China Medical University, Heping District, Nanjing Road No. 155, Shenyang 110001, Liaoning Province, China. liuzhe4321@126.com
Telephone: +86-24-83283330 Fax: +86-24-83283350
Received: January 25, 2016
Peer-review started: January 26, 2016
First decision: May 17, 2016
Revised: May 25, 2016
Accepted: June 14, 2016
Article in press: June 16, 2016
Published online: September 16, 2016
Processing time: 226 Days and 0.5 Hours
Abstract

Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor (E-EWS/pPNET) is a rare aggressive malignant small round cell tumor. In this report, we present the case of a 15-year-old boy who suffered from acute abdominal pain accompanied by hematemesis and melena, and was eventually diagnosed with E-EWS/pPNET. To date, there have been only five reported cases of E-EWS/pPNET of the small bowel including the patient in this report. To the best of our knowledge, this is the first documentation of a pPNET of the small bowel mesentery at nonage. All these have made this report rare and significant.

Keywords: Extraskeletal Ewing’s sarcoma; Peripheral primitive neuroectodermal tumor; Nonage; Small bowel mesentery; Spontaneous rupture

Core tip: Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumors (E-EWS/pPNETs) are rare aggressive malignant small round cell tumors that are derived from the outer central and autonomic nervous systems. To date, there have been only five reported cases of E-EWS/pPNET of the small bowel including the patient presented in this report. The patient presented in this report is the youngest and had the worst prognosis.

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