Metastatic clear cell sarcoma of the pancreas: A rare case report

Abstract

BACKGROUND

Clear cell sarcoma (CCS) is a rare soft-tissue sarcoma. The most common metastatic sites for CCS are the lungs, bones and brain. CCS is highly invasive and mainly metastasizes to the lung, followed by the bone and brain; however, pancreatic metastasis is relatively rare.

CASE SUMMARY

We report on a rare case of CCS with pancreatic metastasis in a 47-year-old man. The patient had a relevant medical history 3 years ago, with abdominal pain as the main clinical manifestation. No abnormalities were observed on physical examination and the tumor was found on abdominal computed tomography. Based on the medical history and postoperative pathology, the patient was diagnosed with CCS with pancreatic metastasis. The patient was successfully treated with surgical interventions, including distal pancreatectomy and splenectomy.

CONCLUSION

This report summarizes the available treatment modalities for CCS and the importance of regular postoperative follow-up for patients with CCS.

Keywords: Clear cell sarcoma; Pancreas; Metastasis; Follow-up; Case report

Core Tip: Clear cell sarcoma (CCS) is a rare soft tissue sarcoma accounting for less than 1% of sarcomas and was originally reported in 1965. CCS is a type of highly invasive cancer which mainly metastasizes to the lungs, followed by the bones and brain, but pancreatic metastasis is relatively rare. Here, we give details of the clinical manifestations and imaging features of a case of metastatic CCS of the pancreas.