Published online Nov 6, 2024. doi: 10.12998/wjcc.v12.i31.6486
Revised: August 19, 2024
Accepted: August 28, 2024
Published online: November 6, 2024
Processing time: 125 Days and 19.6 Hours
Primary cutaneous anaplastic large cell lymphoma (PC-ALCL) poses significant diagnostic difficulties due to its similarity in the appearance of skin lesions with chronic inflammatory disorders and other dermatological conditions. This study aims to investigate these challenges by conducting a comprehensive analysis of a case presenting with PC-ALCL, emphasizing the necessity of accurate differentiation for appropriate management.
An 89-year-old female patient with diabetes and hypertension presented with arm and abdominal ulcerated mass lesions. Diagnostic procedures included skin biopsies, histopathological assessments, and immunohistochemistry, complemented by advanced imaging techniques to confirm the diagnosis. The patient’s lesions were determined as PC-ALCL, characterized by necrosis, chronic inflammation, and a distinct immunophenotypic profile, including CD30, CD3, CD4, and EBER, CD56, MUM-1, Ki 67-positive in > 80% of tumor cells, CD10, but negative for anaplastic lymphoma kinase, CD5, CD20, PAX-5, Bcl-2, Bcl-6, CD8, and CD15. Recurrence was not reported at the 6-month follow-up.
Accurate PC-ALCL differentiation from similar conditions is crucial for effective management and requires a multidisciplinary approach.
Core Tip: This case report describes the diagnostic complexities and management strategies for primary cutaneous anaplastic large cell lymphoma (PC-ALCL), emphasizing the difficulties posed by its necrosis and chronic inflammation presentation. This report underscores the necessity of distinguishing PC-ALCL from similar chronic inflammatory conditions by detailing a patient’s journey from initial misdiagnosis to the tailored multidisciplinary approach that follows. This case illustrates the critical role of precise diagnostic techniques in guiding effective treatment plans for dermatological malignancies through histopathological examinations and immunophenotyping.