Published online Jan 21, 2022. doi: 10.12998/wjcc.v10.i3.1000
Peer-review started: April 22, 2021
First decision: June 24, 2021
Revised: July 7, 2021
Accepted: December 21, 2021
Article in press: December 21, 2021
Published online: January 21, 2022
Processing time: 267 Days and 14.7 Hours
Intraductal papillary neoplasm of the bile duct (IPNB) rarely recurs in a multicentric manner. We encountered a patient with multiple recurrences of the gastric subtype of IPNB one year after spontaneous detachment of the primary tumor during peroral cholangioscopy (POCS).
A 68-year-old woman on maintenance hemodialysis because of lupus nephritis had several cardiovascular diseases and a pancreatic intraductal papillary mucinous neoplasm (IPMN). She was referred to our department for dilation of the common bile duct (CBD) and a tumor in the lumen, detected using ultrasonography. She had no complaints, and blood tests of hepatobiliary enzymes were normal. Magnetic resonance cholangiopancreatography (MRCP) showed a papillary tumor in the CBD with a filling defect detected using endoscopic retrograde cholangiography (ERC). Intraductal ultrasonography revealed a papillary tumor and stalk at the CBD. During POCS, the tumor spontaneously detached with its stalk into the CBD. Pathology showed low-intermediate nuclear atypia of the gastric subtype of IPNB. After 1 year, follow-up MRCP showed multiple tumors distributed from the left hepatic duct to the CBD. ERC and POCS showed multicentric tumors. She was alive without hepatobiliary symptoms at least two years after initial diagnosis of IPNB.
The patient experienced gastric subtype of IPNB without curative resection. Observation may be reasonable for patients with this subtype.
Core Tip: Multiple occurrences of intraductal papillary neoplasm of bile duct (IPNB) are rare. Here we present the case of a patient with multicentric recurrence of IPNB after spontaneous detachment of the primary tumor. She harbored an asynchronous intraductal papillary mucinous neoplasm and experienced gastric subtype of IPNB without complete resection.