Published online Jul 6, 2022. doi: 10.12998/wjcc.v10.i19.6595
Peer-review started: November 27, 2021
First decision: January 12, 2022
Revised: January 24, 2021
Accepted: May 16, 2022
Article in press: May 16, 2021
Published online: July 6, 2022
Processing time: 209 Days and 5 Hours
Extraskeletal Ewing sarcoma (EES) is a member of the Ewing sarcoma family of tumors which is pathologically known as a small, round, blue cell tumor involving bone and soft tissue. The prevalence of EES is only 15%-25% of all Ewing sarcoma and EES often occurs in patients aged from 20-mo-old to 30-years-old resulting in an unfavorable prognosis.
The present case report described a 7-year-old patient with a palpable EES mass of 33 mm × 27 mm × 28 mm in the deep neck with symptoms of persistent dyspnea over the past 5 mo. After laboratory examinations, abnormal physiological and biochemical indicators were not found. Ultrasound images presented the mass to be complex, solid and fluid-filled with circumscribed margins and posterior acoustic enhancement. The mass also presented with partial internal vascularity. The contrast-enhanced magnetic resonance imaging scan illustrated the outstanding enhancement with fast perfusion mode in the early arterial phase.
Our study suggested that a quick-growing mass in the pediatric patient is possibly a malignant tumor whether the mass has well-defined margins or not.
Core Tip: The depth, growth rate and solitary location are valuable indicators for the pre-operative diagnosis of Extraskeletal Ewing sarcoma (EES). Meanwhile, the serpentine-like vascularity was present inside EES, accompanied by the outstanding enhancement with fast perfusion mode in the early arterial phase on the contrast-enhanced magnetic resonance imaging. Multimodal imaging is helpful for clarifying the tumor stage and follow-up.