Published online Apr 16, 2022. doi: 10.12998/wjcc.v10.i11.3630
Peer-review started: December 14, 2021
First decision: January 25, 2022
Revised: February 2, 2022
Accepted: February 27, 2022
Article in press: February 27, 2022
Published online: April 16, 2022
Processing time: 114 Days and 23 Hours
Myoepithelial carcinoma (MC) is a clinically rare malignancy, there is controversy regarding its etiology and its biological behavior is not fully elucidated. Extensive surgical resection is the main treatment method. We describe a case of pleomorphic adenoma (PA) with multiple postoperative recurrences after malignant transformation, and the history of the disease in this patient was more than 20 years. Complete resection during the first surgery of PA and long-term postoperative follow-up is necessary.
A 34-year-old male with PA and a history of 5 postoperative recurrences over 21 years, each surgically removed, presented 15 d ago with headache, nasal congestion, protrusion of the right eyeball and loss of vision in the right eye, with progressively worsening symptoms. The patient underwent surgery, and MC was confirmed by pathology examination. A small PA component was locally visible under light microscope. The patient had a recurrence of the tumor 2 mo after surgery and underwent surgical resection.
During the first operation for PA, care should be taken not to rupture the envelope to prevent tumor cell implantation, and when complete resection is not possible due to the anatomical site, postoperative radiotherapy is necessary to control the lesion and prevent infiltration and malignant transformation of the tumor to MC. Computed tomography and magnetic resonance imaging is important for establishing diagnosis and developing a treatment plan.
Core Tip: This case illustrates that pleomorphic adenoma should be completely removed during the first operation to prevent capsule rupture and tumor cell implantation. When complete resection is not possible due to the anatomical site, postoperative radiotherapy should be performed to control the lesion and prevent infiltration and malignant transformation to myoepithelial carcinoma. Postoperative follow-up, especially long-term follow-up for recurrent cases, is necessary and systemic examination should be undertaken to prevent distant metastasis.