TFE3-expressing malignant perivascular epithelioid cell tumor of the mesentery: A case report and review of literature

Table 1 Clinicopathologic features of mesenteric perivascular epithelioid cell tumor described previous and in present reports

No.	Ref.	Age/sex	Diagnosis	Size (cm)	Nuclear grade	Cellularity	MF / 50 HPF	Invasion	Necrosis	LN status	Morphology	Treatment	Outcome
1	Folpe et al[5]	67/F	PEComa with UMP	13	High	Moderate	0	No	No	Uninvolved	Epithelioid	SE only	NED at 84 months
2		97/F	PEComa	4	Intermediate	Moderate	0	No	No	Uninvolved	Epithelioid	SE only	NED at 38 months
3		80/F	Malignant PEComa	9.5	High	High	> 50	Vascular invasion	Yes	Uninvolved	Epithelioid and spindle	SE only	NED at 19 months
4		46/F	Malignant PEComa	12	Intermediate	Moderate	5	Vascular invasion	Yes	Uninvolved	Epithelioid	SE+CT	Recur and liver metastases at 22 months; die at 27 months
5	Gross et al[6]	5.5/M	Malignant PEComa	5	High	Moderate	NA	Surrounding tissue invasion	No	Uninvolved	Spindle	SE only	NED at 24 months
6	Lai et al[7]	59/M	Malignant PEComa	11	High	High	3	Vascular invasion	Yes	Uninvolved	Epithelioid and spindle	SE+CT	Recur at 6 months; alive
7	Fu et al[8]	38/F	Malignant PEComa	10	Intermediate	Moderate	2	Surrounding tissue invasion	Yes	Involved		SE+CT	NED at 6 months
8	Shi et al[9]	48/F	Malignant PEComa	14	High	High	Elevated	No	Yes	Uninvolved	Epithelioid	SE+CT	NED at 60 months
9	Wejman et al[10]	67/F	PEComa	3.5	Mild	Moderate	1-2	No	No	Uninvolved	Epithelioid and spindle	SE+CT	NA
10	Present case	50/F	Malignant PEComa	8	High	High	40	Surrounding tissue invasion	Yes	Uninvolved	Epithelioid and spindle	SE+CT	NED at 6 months

MF: Mitotic figure; HPF: High power field; LN: Lymph node; M: Male; F: Female; PEComa: Perivascular epithelioid cell tumor; UMP: Unknown malignant potential; SE: Surgical excision; NED: No evidence of disease; CT: Chemotherapy; NA: Not available.