Published online Aug 26, 2020. doi: 10.4330/wjc.v12.i8.427
Peer-review started: March 24, 2020
First decision: April 26, 2020
Revised: June 8, 2020
Accepted: July 19, 2020
Article in press: July 19, 2020
Published online: August 26, 2020
Processing time: 146 Days and 8.4 Hours
Treatment of congenitally corrected transposition of great arteries (cc-TGA) with anatomic repair strategy has been considered superior due to restoration of the morphologic left ventricle in the systemic circulation. However, data on long term outcomes are limited to single center reports and include small sample sizes.
To perform a systematic review and meta-analysis for observational studies reporting outcomes on anatomic repair for cc-TGA.
MEDLINE and Scopus databases were queried using predefined criteria for reports published till December 31, 2017. Studies reporting anatomic repair of minimum 5 cc-TGA patients with at least a 2 year follow up were included. Meta-analysis was performed using Comprehensive meta-analysis v3.0 software.
Eight hundred and ninety-five patients underwent anatomic repair with a pooled follow-up of 5457.2 patient-years (PY). Pooled estimate for operative mortality was 8.3% [95% confidence interval (CI): 6.0%-11.4%]. 0.2% (CI: 0.1%-0.4%) patients required mechanical circulatory support postoperatively and 1.7% (CI: 1.1%-2.4%) developed post-operative atrioventricular block requiring a pacemaker. Patients surviving initial surgery had a transplant free survival of 92.5% (CI: 89.5%-95.4%) per 100 PY and a low rate of need for pacemaker (0.3/100 PY; CI: 0.1-0.4). 84.7% patients (CI: 79.6%-89.9%) were found to be in New York Heart Association (NYHA) functional class I or II after 100 PY follow up. Total re-intervention rate was 5.3 per 100 PY (CI: 3.8-6.8).
Operative mortality with anatomic repair strategy for cc-TGA is high. Despite that, transplant free survival after anatomic repair for cc-TGA patients is highly favorable. Majority of patients maintain NYHA I/II functional class. However, monitoring for burden of re-interventions specific for operation type is very essential.
Core tip: This is a systematic review and meta-analysis looking at short- and long-term outcomes with the anatomic repair strategy (double switch or atrial switch Rastelli operation) for patients with congenitally corrected transposition of great arteries. Updated outcomes of operative mortality, long term survival free of transplantation and re-operation/re-intervention rates are provided. We find favorable long-term survival after anatomic repair despite the initial high operative mortality.