Klippel-Trenaunay syndrome with gastrointestinal bleeding, splenic hemangiomas and left inferior vena cava

Figure 1 Cutaneous vascular malformations and abnormal right leg in the patient. A: Cutaneous vascular malformations of the gluteal region and body; B: The enlarged right leg.

Figure 2 Angiograms demonstrate contrast opacification of the superior mesenteric artery and its branches. A: Some abnormal small veins that were filled earlier in the arterial phase; B: Manipulus contrast extravasation into the terminal ileum; C: Abnormal ectatic slow-emptying veins and extravasation of contrast material after superselective catheterization; D: No active bleeding after superselective vessel embolism with gelfoam.

Figure 3 Lesions of gastrointestinal tract on endoscopy. A: Gastroscopy shows multiple polypoid mucosal nodules with abundant vasculature which had a purplish red chrysanthemum-like surface, which are centrally located at the greater curvature of the gastric antrum and gastric corpus; B: Colonoscopy shows several polypoid mass lesions with abundant vasculature, which are centrally located from the terminal ileum to the descending colon; C: Capsule endoscopy revealing several vascular malformation lesions distributing over the jejunum and ileum.

Figure 4 Contrast-enhanced abdominal computed tomography (CT) showing splenic hemangiomas (A) and left inferior vena cava (IVC) (B).