Case Report
Copyright ©The Author(s) 2020. Published by Baishideng Publishing Group Inc. All rights reserved.
World J Gastroenterol. Dec 28, 2020; 26(48): 7707-7718
Published online Dec 28, 2020. doi: 10.3748/wjg.v26.i48.7707
Primary intestinal lymphangiectasia in an adult patient: A case report and review of literature
Rudolf Huber, Georg Semmler, Alexander Mayr, Felix Offner, Christian Datz
Rudolf Huber, Georg Semmler, Alexander Mayr, Christian Datz, Department of Internal Medicine, General Hospital Oberndorf, Teaching Hospital of the Paracelsus Medical University Salzburg, Oberndorf 5110, Austria
Felix Offner, Department of Pathology, General Hospital Feldkirch, Feldkirch 6800, Austria
Author contributions: Huber R, Mayr A, Datz C and Offner F contributed to patient management and histological evaluation; Huber R, Semmler G and Datz C contributed to literature review and drafting of the manuscript. All authors contributed to revision for important intellectual content and approved the final version of the manuscript.
Informed consent statement: The patient consented to her case being published anonymously.
Conflict-of-interest statement: The authors declare that they have no conflicts of interest regarding the submitted work. However, the following authors declare conflicts of interest outside the submitted work: Christian Datz serves as an advisory board member of SPAR Österreich Warenhandels AG.
CARE Checklist (2016) statement: The authors have read the CARE Checklist (2016), and the manuscript was prepared and revised according to the CARE Checklist (2016).
Open-Access: This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/Licenses/by-nc/4.0/
Corresponding author: Christian Datz, MD, Professor, Department of Internal Medicine, General Hospital Oberndorf, Teaching Hospital of the Paracelsus Medical University Salzburg, Paracelsusstraße 37, Oberndorf 5110, Austria. c.datz@kh-oberndorf.at
Received: October 2, 2020
Peer-review started: October 2, 2020
First decision: November 23, 2020
Revised: November 29, 2020
Accepted: December 6, 2020
Article in press: December 6, 2020
Published online: December 28, 2020
Processing time: 76 Days and 21.4 Hours
Core Tip

Core Tip: Although Primary intestinal lymphangiectasia usually develops in early childhood, we present the case of a 34-year-old woman. We observed a striking collinearity with female hormone status in our patient, presenting a potential area of future research. Moreover, we performed a literature review of all published case reports so far and systematically assessed clinical presentation to provide a practical approach to facilitate diagnosis and therapy of primary intestinal lymphangiectasia in adults for the first time.