Published online May 14, 2015. doi: 10.3748/wjg.v21.i18.5735
Peer-review started: November 18, 2014
First decision: December 26, 2014
Revised: January 25, 2015
Accepted: February 11, 2015
Article in press: February 11, 2015
Published online: May 14, 2015
Processing time: 182 Days and 8.1 Hours
A 41-year-old man with a continuous-flow left ventricular assist device presented for evaluation of dysphagia and dark urine. He was found to have a significantly elevated L-lactate dehydrogenase and an elevated plasma free hemoglobin consistent with intravascular hemolysis. After the hemolysis ceased, both the black urine and dysphagia resolved spontaneously. Transient esophageal dysfunction, as a manifestation of gastrointestinal dysmotility, is known to occur in the setting of hemolysis. Paroxysmal nocturnal hemoglobinuria is another recognized cause of massive hemolysis with gastrointestinal dysmotility occurring in 25%-35% of patients during a paroxysm. Intravascular hemolysis increases plasma free hemoglobin, which scavenges nitric oxide (NO), an important second messenger for smooth muscle cell relaxation. The decrease in NO can lead to esophageal spasm and resultant dysphagia. In our patient the resolution of hemolysis resulted in resolution of dysphagia.
Core tip: Transient esophageal dysfunction, as a manifestation of gastrointestinal dysmotility, is known to occur in the setting of hemolysis. We present a case of dysphagia secondary to hemolysis caused by a continuous-flow left ventricular assist device. Our case report aims to bring this etiology of dysphagia to the attention of gastroenterologists and cardiologists to limit invasive investigations in these patients and highlight the possibility that hemolysis may serve as an early indicator of pump thrombosis and adverse outcomes.