Editorial
Copyright ©2007 Baishideng Publishing Group Co., Limited. All rights reserved.
World J Gastroenterol. May 21, 2007; 13(19): 2649-2654
Published online May 21, 2007. doi: 10.3748/wjg.v13.i19.2649
Genotype phenotype classification of hepatocellular adenoma
Paulette Bioulac-Sage, Jean Frédéric Blanc, Sandra Rebouissou, Charles Balabaud, Jessica Zucman-Rossi
Paulette Bioulac-Sage, CHU Bordeaux, Hôpital Pellegrin, Department of Pathology, Bordeaux F-33076, France
Paulette Bioulac-Sage, Jean Frédéric Blanc, Charles Balabaud, Inserm, U889, Bordeaux F-33076, GREF; Univ Victor Segalen Bordeaux 2, Bordeaux F-33076, France
Jean Frédéric Blanc, Charles Balabaud, CHU Bordeaux, Hôpital Saint André, Department of Hepatology, Bordeaux F-33075, France
Sandra Rebouissou, Jessica Zucman-Rossi, Inserm, U674, CEPH, Univ Paris 7, Paris F-75010, France
Author contributions: All authors contributed equally to the work.
Correspondence to: Paulette Bioulac-Sage, CHU Bordeaux, Hôpital Pellegrin, Department of Pathology, Place Amélie Raba Léon, Bordeaux cedex F-33076, France. paulette.bioulac-sage@chu-bordeaux.fr
Telephone: +33-5-57571771 Fax: +33-5-56514077
Received: March 14, 2007
Revised: March 18, 2007
Accepted: March 23, 2007
Published online: May 21, 2007
Abstract

Studies that compare tumor genotype with phenotype have provided the basis of a new histological/molecular classification of hepatocellular adenomas. Based on two molecular criteria (presence of a TCF1/HNF1α or β-catenin mutation), and an additional histological criterion (presence or absence of an inflammatory infiltrate), subgroups of hepatocellular adenoma can be defined and distinguished from focal nodular hyperplasia. Analysis of 96 hepatocellular adenomas performed by a French collaborative network showed that they can be divided into four broad subgroups: the first one is defined by the presence of mutations in TCF1 gene inactivating the hepatocyte nuclear factor 1 (HNF1α); the second by the presence of β-catenin activating mutations; the category without mutations of HNF1α or β-catenin is further divided into 2 subgroups depending on the presence or absence of inflammation. Therefore, the approach to the diagnosis of problematic benign hepatocytic nodules may be entering a new era directed by new molecular information. It is hoped that immunohistological tools will improve significantly diagnosis of liver biopsy in our ability to distinguish hepatocellular adenoma from focal nodular hyperplasia (FNH), and to delineate clinically meaningful entities within each group to define the best clinical management. The optimal care of patients with a liver nodule will benefit from the recent knowledge coming from molecular biology and the combined expertise of hepatologists, pathologists, radiologists, and surgeons.

Keywords: Hepatocellular adenoma; HNF1α mutation; β-catenin mutation; Inflammatory adenoma; Telangiectatic adenoma; Maturity-onset diabetes of the young; Hepatocyte nuclear factor 1; CTNNB1; Focal nodular hyperplasia