Incidental meandering right pulmonary vein, literature review and proposed nomenclature revision

Table 1 Published cases of meandering pulmonary vein

Ref.	Gender	Age (yr)	Symptoms	Scimitar sign	Features of scimitar syndrome	Investigations (in addition to CXR)	Anomalous pulmonary venous drainage	Original diagnosis	Proposed diagnosis
Morgan et al[4]	M	22	Incidental	Y	Thoracic aorta supply, right lung hypoplasia, dextroposition	Pulmonary angiography and cardiac catheterization	Single right pulmonary vein to left atrium	Scimitar syndrome with normal pulmonary venous drainage	AUSPV
Goodman et al[7]	F	51	Haemoptysis	Y	Dextroposition, right pulmonary artery hypoplasia	Pulmonary angiography and cardiac catheterization	Single right pulmonary vein to left atrium	MRPV	AUSPV
Kanemoto et al[15]	F	48	Orthopnea and productive cough	Y	Right lung hypoplasia, dextroposition	Lung perfusion, CT, ECHO, Pulmonary angiography	Single right pulmonary vein to left atrium	Pseudo-scimitar sign	AUSPV
Cukier et al[21]	F	27	Haemoptysis	Y	Abdominal aorta supply, right lung hypoplasia	Pulmonary angiography and cardiac catheterization	Inferior right pulmonary vein to left atrium	Scimitar syndrome	MRPV
Holt et al[22]	M	2	Murmur and failure to thrive	Y	Systemic supply, right lung hypoplasia, dextroposition	ECHO, cardiac catheterization	Superior and inferior right pulmonary veins to left atrium	Scimitar syndrome variant	MPVs
Tsitouridis et al[19]	M	41	Incidental	Y	Right lung hypoplasia, dextroposition	CT	Single right pulmonary vein to left atrium	MPV	AUSPV
Yoo et al[20]	F	1	Respiratory distress	Y	Right lung hypoplasia, dextroposition	CT	Single right pulmonary vein to left atrium	MRPV	AUSPV
Siu et al[23]	F	43	Incidental	Y	Dextroposition	ECHO, CT	Single right pulmonary vein to left atrium	Scimitar variant	AUSPV
Current case	F	80	Incidental	Y	Right lung hypoplasia, dextroposition, Hypoplasia right pulmonary artery	CT	Inferior right pulmonary vein to left atrium	MRPV	MRPV
Collins et al[8]	M	20	Incidental	Y	-	ECHO, cardiac catheterization, pulmonary angiography	All 4 pulmonary veins to left atrium	Idiopathic prominence of pulmonary veins	MPVs
Takeda et al[11]	F	28	Incidental	Y	-	Pulmonary angiography	NS	Scimitar variant	-1
Kriss et al[9]	F	12	Incidental	Y	-	CT, cardiac catheterization, pulmonary angiography	Right superior and inferior and left inferior pulmonary veins to left atrium	MPV	MPVs
Salazar-Mena et al[14]	F	15	Incidental	Y	-	Pulmonary angiography and cardiac catheterization	Right inferior pulmonary vein to left atrium	MRPV	MRPV
Al-Naami et al[24]	M	2/12	Failure to thrive, ASD, VSD	N2	-	ECHO, CT, cardiac catheterization	Right inferior pulmonary vein to left atrium	MPV	MRPV

¹Unable to name due to lack of details in article.

²Chest X-ray demonstrated cardiomegaly and congested lung fields which may have masked the scimitar sign. M: Male; F: Female; NS: Not stated in article; ASD: Atrial septal defect; AUSPV: Anomalous unilateral single pulmonary vein; CT: Computed tomography; CXR: Chest X-ray; ECHO: Echocardiogram; MPV: Meandering pulmonary vein; MRPV: Meandering right pulmonary vein; VSD: Ventricular septal defect; N: No; Y: Yes.