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©The Author(s) 2015. Published by Baishideng Publishing Group Inc. All rights reserved.
World J Gastrointest Surg. Mar 27, 2015; 7(3): 25-32
Published online Mar 27, 2015. doi: 10.4240/wjgs.v7.i3.25
Colorectal cancer risk in hamartomatous polyposis syndromes
Fábio Guilherme Campos, Marleny Novaes Figueiredo, Carlos Augusto Real Martinez
Fábio Guilherme Campos, Surgery at University of São Paulo, Medical School, São Paulo SP 01411-000, Brazil
Fábio Guilherme Campos, Colorectal Surgery Division, Gastroenterology Department, Hospital das Clínicas, University of São Paulo, Medical School, São Paulo SP 01411-000, Brazil
Marleny Novaes Figueiredo, Colorectal Surgery Division, University of São Paulo, Medical School, São Paulo SP 01411-000, Brazil
Carlos Augusto Real Martinez, Surgery at University of Campinas, Medical School (UNICAMP), São Paulo 01411-000, Brazil
Carlos Augusto Real Martinez, Colorectal Surgery Division, Gastrocentro Hospital, University of Campinas, Medical School, São Paulo 01411-000, Brazil
Author contributions: All authors contributed equally in performing literature search and analysing results; Campos FG wrote the manuscript.
Conflict-of-interest: All authors declare no conflicts of interest (including commercial, personal, political, intellectual, or religious interests.
Correspondence to: Fábio Guilherme Campos, MD, Colorectal Surgery Division, Gastroenterology Department, Hospital das Clínicas, University of São Paulo, Medical School, Rua Padre João Manoel, 222 Cj 120, São Paulo SP 01411-000, Brazil. fgmcampos@terra.com.br
Telephone: +55-11-30647010 Fax: +55-11-30610108
Received: September 24, 2014
Peer-review started: September 24, 2014
First decision: December 17, 2014
Revised: January 6, 2015
Accepted: February 4, 2015
Article in press: February 9, 2015
Published online: March 27, 2015
Processing time: 188 Days and 5.8 Hours
Core Tip

Core tip: This is a brief review about clinical presentation, diagnosis, molecular features and surveillance recommendations regarding hamartomatous polyposis syndromes: Peutz-jeghers syndrome, juvenil polyposis Syndrome and PTEN Hamartoma Tumor Syndrome (Bannayan-Riley-Ruvalacaba and Cowden Syndromes).