Nationwide questionnaire survey on pediatric pancreatic tumors in Japan

Figure 1 Distribution of cases per institution. Over the 22-year period, 75 of 145 institutions (51.7%) reported zero cases, 55 institutions (37.9%) reported 1-4 cases, and 11 institutions (7.6%) reported 5-9 cases. Four institutions (2.8%) managed > 10 cases, with only one of these institutions reporting > 20 cases. The number of cases experienced varies greatly from facility to facility.

Figure 2 Questionnaire results. In the primary survey, 228 cases were enrolled, and 213 cases were finally enrolled in the secondary survey.

Figure 3 Diagnoses and procedures performed in the 213 cases. A: Diagnoses of the 213 cases. The most common type of pancreatic tumor was SPN [n = 164 (77.0%)], followed by pancreatoblastoma [n = 16 (7.5%)], pancreatic endocrine tumor [n = 14 (6.6%)], non-epithelial tumor [n = 9 (4.2%)], pancreatic cancer [n = 7 (3.3%)], and metastatic pancreatic tumor [n = 3 (1.4%)]; B: Procedures performed in the 213 cases. In total, 123 (57.7%) patients underwent distal pancreatectomy, of whom 49 underwent laparoscopic surgery. Furthermore, 44 (20.7%) patients underwent enucleation, of whom eight underwent laparoscopic surgery. In total, 32 (15.0%) patients underwent pancreaticoduodenectomy, of whom one underwent laparoscopic surgery. Moreover, one patient underwent total pancreatectomy, and the remaining 13 patients underwent other procedures. Of them, one patient had laparoscopic surgery.