Absent inferior vena cava combined with idiopathic noncirrhotic portal hypertension resulting esophagogastric variceal bleeding: A case report

Figure 1 Absence of the hepatic segment of the inferior vena cava complicated by noncirrhotic portal hypertension with esophagogastric varices. A: Three-dimensional volume-rendered computed tomography reconstruction demonstration of the absence of the hepatic segment of the inferior vena cava with azygos continuation; B: Esophagogastroduodenography showed large proximal esophageal varices with positive red wale signs; C: The liver pathological feature revealed moderate fibrosis in portal areas with absent portal vein lumens, and no evidence of perisinusoidal fibrosis or hepatic veno-occlusive disease.

Figure 2 Esophagogastric varices significantly improved after two sessions of endoscopic band ligation therapy. A: Pretreatment: Large esophageal varices (grade III) with red wale signs; B: Post-second ligation: Large esophageal varices reduced in size in comparison to the precious evaluation; C: Two-month follow-up showed status post endoscopic band ligation, with excellent resolution of esophageal varices.