Copyright
©The Author(s) 2020.
World J Gastroenterol. Aug 21, 2020; 26(31): 4718-4728
Published online Aug 21, 2020. doi: 10.3748/wjg.v26.i31.4718
Published online Aug 21, 2020. doi: 10.3748/wjg.v26.i31.4718
Table 1 Literature search results and analyzed manuscripts
Ref. | Country | Year of publication | Type of study | n of reported patients | n of cancer (%) |
Ammori et al[27] | United Kingdom | 2002 | Single-center, retrospective | 8 | 3 (37.5) |
De Kerckhove et al[19] | Belgium | 2005 | ELTR registry, retrospective | 113 | 3 (2.7) |
Kassahun et al[21] | Germany | 2005 | Single-center, retrospective | 33 | 3 (9) |
Habib et al[17] | United States | 2006 | Single-center, retrospective | 33 | 1 (3) |
Bockhorn et al[30] | Germany | 2006 | Single-center, retrospective | 12 | 3 (25) |
Millwala et al[5] | United States | 2008 | UNOS registry, retrospective | 104 | 3 (2.9) |
Ulrich et al[3] | Germany | 2008 | Single-center, retrospective | 44 | 4 (9) |
Hori et al[24] | Japan | 2010 | Single-center, retrospective | 5 | 1 (20) |
Lendoire et al[13] | Argentina | 2011 | Multicenter, retrospective | 24 | 1 (4.2) |
Mabrut et al[20] | France | 2013 | Multicenter, retrospective | 155 | 8 (5) |
Moslim et al[12] | United States | 2015 | Single-center, retrospective | 9 | 3 (33.3) |
Fahrner et al[25] | Germany | 2018 | Single-center, retrospective | 21 | 4 (19) |
Table 2 Diagnostic work flow prior to surgery
Ref. | CT | MRI | ERCP | Ultrasound | Others |
Ammori et al[27] | Yes | Yes | 100% | Yes | No data |
De Kerckhove et al[19] | Yes | Yes | Yes | Yes | Percutaneous cholangiography |
Kassahun et al[21] | 100% | 16.2% | 83.9% | 100% | No data |
Habib et al[17] | No data | No data | No data | No data | No data |
Bockhorn et al[30] | 100% | No data | 92% | 100% | No data |
Millwala et al[5] | No data | No data | No data | No data | No data |
Ulrich et al[3] | Yes | Yes | Yes | Yes | Percutaneous cholangiography |
Hori et al[24] | No data | No data | No data | No data | No data |
Lendoire et al[13] | Yes | Yes | Yes | Yes | Percutaneous cholangiography |
Mabrut et al[20] | No data | 74.7% | 27.7% | No data | No data |
Moslim et al[12] | No data | No data | No data | No data | No data |
Fahrner et al[25] | No data | No data | No data | No data | No data |
Table 3 Patient demographics, duration of disease and tumor identification
Ref. | Age (yr) | Female sex (%) | Duration of disease | Tumor identification |
Ammori et al[27] | 35 | 75 | No data | No data |
De Kerckhove et al[19] | 39.7 | 52 | No data | No data |
Kassahun et al[21] | 51.5 | 55 | < 1 yr 51%, 1-5 yr 13%, > 5 yr 35% | No data |
Habib et al[17] | 26 | 50 | No data | No data |
Bockhorn et al[30] | 39 | 42 | No data | 67% incidental finding |
Millwala et al[5] | 35 | 55 | No data | No data |
Ulrich et al[3] | 49 | 55 | < 1 yr 55%, > 5 yr 2.5% | 100% incidental finding |
Hori et al[24] | 23.74 | No data | 6.4 yr | 100% puncture of nodule prior surgery |
Lendoire et al[13] | 48.7 | 70 | 2.6 yr | 100% incidental finding |
Mabrut et al[20] | 55.7 | 43 | 7 mo | No data |
Moslim et al[12] | 40 | 22 | No data | 100% incidental finding |
Fahrner et al[25] | 56 | 74 | No data | 75% incidental finding 25% suspicious nodules in diagnostics |
Table 4 Surgical treatment, tumor characteristics and survival
Ref. | Surgery for all patients (LR vs OLT)1 | TNM | 1-yr survival cancer patients | Recurrence |
Ammori et al[27] | 50% vs 50% | No data | 33% | 0% |
De Kerckhove et al[19] | 0% vs 100% | No data | 66% | 33% |
Kassahun et al[21] | 87% vs 0% | No data | 0% | 33% |
Habib et al[17] | 0% vs 100% | No data | 0% | No data |
Bockhorn et al[30] | 83% vs 17% | n = 1 pT1, n = 1 pT2 | 66% | 0% |
Millwala et al[5] | 0% vs 100% | No data | 0% | No data |
Ulrich et al[3] | 90% vs 10% | No data | 0% | No data |
Hori et al[24] | 0% vs 100% | No data | No data | No data |
Lendoire et al[13] | 91.6% vs 0% | No data | 100% | No data |
Mabrut et al[20] | 75% vs 18.9% | n = 6 R0, n = 1 peritoneal seeding | 33% | 50% |
Moslim et al[12] | 22% vs 78% | No data | 0% | 33%, 66% tumor progression |
Fahrner et al[25] | 90% vs 10% | n = 1 pT1N1, n = 2 pT2, n = 1 pT3 | 100% | 75% |
- Citation: Fahrner R, Dennler SG, Inderbitzin D. Risk of malignancy in Caroli disease and syndrome: A systematic review. World J Gastroenterol 2020; 26(31): 4718-4728
- URL: https://www.wjgnet.com/1007-9327/full/v26/i31/4718.htm
- DOI: https://dx.doi.org/10.3748/wjg.v26.i31.4718