Giant primary angiosarcoma of the small intestine showing severe sepsis

Table 1 Overview of the literature on primary angiosarcoma of the small intestine since 2000

	Author	Patient (age/sex)	Tumor manifestation	Tumor size (cm)	Histology	Symptoms	Therapy	Outcome
	Report year
1	Delvaux et al	67/M	Jejunum ileum	2.2	Epithelioid	Melena	Resection	Died 3 mo after
	2000					Abdominal pain		Operation
2	Fraiman et al	85/M	Small intestine	8-10	High-grade	Weight loss	Resection	Survived
	2003					Decreased appetite	Chemotherapy	At least 1 yr
3	Keleman et al	76/M	Ileum	NA	Mixed,well-differentiated and epithelioid	Abdominal pain	Resection	Died 9 d after
	2004					Poor appetite		Operation
4	Allison et al	84/F	Jejunum	NA	Epithelioid	Anemia	NA	Died 17 mo after
	2004					Shortness of breath		Diagnosis
5	Allison et al	47/M	Jejunum	NA	Epithelioid	Anemia	NA	Died 4 mo after
	2004					Shortness of breath		Diagnosis
6	Butrón Vila et al	70/M	Ileum	5	Mixed, well-differentiated and epithelioid	Abdominal pain	Resection	Survived
	2005					Vomiting	Chemotherapy	At least 4 yr
							Radiation
7	Al Ali et al	87/M	Jejunum (and duodenum)	NA	Epithelioid	Lethargy, weakness	Endoscopy,	Died 6 wk after
	2006					Chest pain	Argon Plasma coagulation	Diagnosis
8	Policarpio-Nicolas et al	51/F	Terminal ileum	NA	Well-differentiated	Decreased appetite	Resection and	Died 10 mo after
	2006					Vague abdominal pain	Palliative care	Operation
9	Grewal et al	73/M	Jejunum (and duodenum)	NA	Epithelioid	Weakness, anemia	Resection	Died 4 mo after
	2008					Melena		Operation
10	Turan et al	NA/M	Jejunum	NA	NA	Acute abdominal signs	Resection	Died 3 yr after
	2010						Chemotherapy	Operation
11	Zacarias Föhrding et al	84/M	Small intestine	NA	Epithelioid	Anemia, melena	Resection	Died from intracranial
	2012							Hemorrhage
12	Our case	85/F	Small intestine	24 × 17.5 × 18	High-grade	Sepsis	Resection	Died 42 d after
								operation

Modified from Zacarias Föhrding et al[6]. Overview of the literature on primary angiosarcoma of the small intestine since 2000. NA: Not available; M: Male; F: Female.