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Cited by in CrossRef
For: Fahrner R, Dennler SG, Inderbitzin D. Risk of malignancy in Caroli disease and syndrome: A systematic review. World J Gastroenterol 2020; 26(31): 4718-4728 [PMID: 32884228 DOI: 10.3748/wjg.v26.i31.4718]
URL: https://www.wjgnet.com/1007-9327/full/v26/i31/4718.htm
Number Citing Articles
1
Philipp Heumann, Andreas Albert, Karsten Gülow, Denis Tümen, Martina Müller, Arne Kandulski. Current and Future Therapeutic Targets for Directed Molecular Therapies in CholangiocarcinomaCancers 2024; 16(9) doi: 10.3390/cancers16091690
2
Yusuke Johira, Tomokazu Kawaoka, Shinsuke Uchikawa, Hatsue Fujino, Atsushi Ono, Takashi Nakahara, Eisuke Murakami, Wataru Okamoto, Masami Yamauchi, Masataka Tsuge, Michio Imamura, Hiroshi Aikata, Shiro Oka. Caroli's disease in two siblingsKanzo 2023; 64(2) doi: 10.2957/kanzo.64.66
3
Michael Bitzer, Sabrina Groß, Jörg Albert, Judit Boda-Heggemann, Thomas Brunner, Reiner Caspari, Enrico De Toni, Frank Dombrowski, Matthias Evert, Andreas Geier, Eleni Gkika, Martin Götz, Thomas Helmberger, Ralf-Thorsten Hoffmann, Peter Huppert, Achim Kautz, David Krug, Christian La Fougère, Hauke Lang, Philipp Lenz, Tom Lüdde, Andreas Mahnken, Silvio Nadalin, Hoa Huu Phuc Nguyen, Johann Ockenga, Karl Oldhafer, Philipp Paprottka, Philippe Pereira, Thorsten Persigehl, Ruben Plentz, Jürgen Pohl, Heinrich Recken, Peter Reimer, Jutta Riemer, Ulrike Ritterbusch, Elke Roeb, Jörn Rüssel, Barbara Schellhaas, Peter Schirmacher, Hans Jürgen Schlitt, Irene Schmid, Andreas Schuler, Daniel Seehofer, Marianne Sinn, Andreas Stengel, Christoph Stoll, Andrea Tannapfel, Anne Taubert, Reina Tholen, Jörg Trojan, Ingo van Thiel, Arndt Vogel, Thomas Vogl, Frank Wacker, Oliver Waidmann, Heiner Wedemeyer, Henning Wege, Dane Wildner, Marcus-Alexander Wörns, Peter Galle, Nisar Malek. S3-Leitlinie Diagnostik und Therapie biliärer Karzinome – LangversionZeitschrift für Gastroenterologie 2023; 61(04) doi: 10.1055/a-2026-1240
4
Tsuyoshi Hamada, Yousuke Nakai. Management of Pancreatic Cancer and Cholangiocarcinoma2021;  doi: 10.1007/978-981-16-2870-2_1
5
Michael Bitzer, Sabrina Groß, Jörg Albert, Susanne Blödt, Judit Boda-Heggemann, Thomas Brunner, Reiner Caspari, Enrico De Toni, Frank Dombrowski, Matthias Evert, Markus Follmann, Paul Freudenberger, Cihan Gani, Andreas Geier, Eleni Gkika, Martin Götz, Thomas Helmberger, Ralf-Thorsten Hoffmann, Peter Huppert, David Krug, Christian La Fougère, Hauke Lang, Thomas Langer, Philipp Lenz, Tom Lüdde, Andreas Mahnken, Silvio Nadalin, Hoa Huu Phuc Nguyen, Monika Nothacker, Johann Ockenga, Karl Oldhafer, Philipp Paprottka, Philippe Pereira, Thorsten Persigehl, Ruben Plentz, Jürgen Pohl, Heinrich Recken, Peter Reimer, Jutta Riemer, Ulrike Ritterbusch, Elke Roeb, Jörn Rüssel, Barbara Schellhaas, Peter Schirmacher, Hans Jürgen Schlitt, Irene Schmid, Andreas Schuler, Daniel Seehofer, Marianne Sinn, Andreas Stengel, Nadine Steubesand, Christoph Stoll, Andrea Tannapfel, Anne Taubert, Reina Tholen, Jörg Trojan, Ingo van Thiel, Arndt Vogel, Thomas Vogl, Frank Wacker, Oliver Waidmann, Heiner Wedemeyer, Henning Wege, Dane Wildner, Marcus-Alexander Wörns, Peter Galle, Nisar Malek. S3-Leitlinie „Diagnostik und Therapie des Hepatozellulären Karzinoms“ – Langversion 4.0Zeitschrift für Gastroenterologie 2024; 62(01) doi: 10.1055/a-2189-6353
6
Kedar Sharbidre, Mohd Zahid, Sudhakar Kundapur Venkatesh, Chandra Bhati, Neeraj Lalwani. Imaging of fibropolycystic liver diseaseAbdominal Radiology 2022; 47(7) doi: 10.1007/s00261-022-03565-7
7
Mégane Chenin, Anita Paisant, Jérôme Lebigot, Paul Bazeries, Kawtar Debbi, Maxime Ronot, Valérie Laurent, Christophe Aubé. Cystic liver lesions: a pictorial reviewInsights into Imaging 2022; 13(1) doi: 10.1186/s13244-022-01242-3
8
Sophie H. Chung, Teviah E. Sachs. Choledochal CystsCurrent Problems in Surgery 2024; 61(11) doi: 10.1016/j.cpsurg.2024.101594
9
Michael Bitzer, Sabrina Groß, Jörg Albert, Susanne Blödt, Judit Boda-Heggemann, Katrin Borucki, Thomas Brunner, Reiner Caspari, Frank Dombrowski, Matthias Evert, Markus Follmann, Paul Freudenberger, Cihan Gani, Jamila Gebert, Andreas Geier, Eleni Gkika, Martin Götz, Thomas Helmberger, Ralf-Thorsten Hoffmann, Peter Huppert, David Krug, Christian La Fougère, Hauke Lang, Thomas Langer, Philipp Lenz, Tom Lüdde, Andreas Mahnken, Silvio Nadalin, Hoa Huu Phuc Nguyen, Monika Nothacker, Johann Ockenga, Karl Oldhafer, Julia Ott, Philipp Paprottka, Philippe Pereira, Thorsten Persigehl, Ruben Plentz, Jürgen Pohl, Heinrich Recken, Peter Reimer, Jutta Riemer, Kristina Ringe, Elke Roeb, Jörn Rüssel, Barbara Schellhaas, Peter Schirmacher, Hans Jürgen Schlitt, Irene Schmid, Kerstin Schütte, Andreas Schuler, Daniel Seehofer, Marianne Sinn, Andreas Stengel, Nadine Steubesand, Christoph Stoll, Andrea Tannapfel, Anne Taubert, Jörg Trojan, Ingo van Thiel, Martin Utzig, Arndt Vogel, Thomas Vogl, Frank Wacker, Oliver Waidmann, Heiner Wedemeyer, Henning Wege, Gregor Wenzel, Dane Wildner, Marcus-Alexander Wörns, Peter Galle, Nisar Malek. S3-Leitlinie Diagnostik und Therapie des Hepatozellulären Karzinoms – LangversionZeitschrift für Gastroenterologie 2025; 63(03) doi: 10.1055/a-2460-6298
10
Amr Shaaban Hanafy, Eslam Kamal Fahmy, Rania Naguib, Moaz Abulfaraj, Ahmed F. Omar, Hend Naguib, Mohamed Mahmoud Abdelrahman, Hany A. Elkattawy. Clinical outcomes in Caroli disease and Caroli syndrome: a longitudinal observational cohort studyScientific Reports 2026; 16(1) doi: 10.1038/s41598-026-42855-8
11
Kevin Ka-Wan Chu, Jin He. Rare Liver and Biliary Tract Diseases2026;  doi: 10.1007/978-3-032-15076-9_8
12
Muhammad Nabeel Shafqat, Muhammad Yousuf Y Memon, Salman Javed, Sai Gautham Kanagala, Momina Saleem. Caroli's Syndrome: A Case Report and Literature ReviewCureus 2023;  doi: 10.7759/cureus.50871
13
Gary C. Kanel. Atlas of Liver Pathology2024;  doi: 10.1016/B978-0-323-82533-7.00010-7
14
Luca Filippi, Luca Urso, Orazio Schillaci, Laura Evangelista. Hepato-Biliary Imaging in an Acute Setting: Is There a Role for Nuclear Medicine?Seminars in Nuclear Medicine 2023; 53(6) doi: 10.1053/j.semnuclmed.2023.05.002
15
Christian A. Hudert, Martin Jankofsky, Verena Keitel-Anselmino, Marcin Krawczyk, Andreas Kremer, Frank Lammert, Eberhard Lurz, Petra Lynen, Eva-Doreen Pfister, Christian P. Strassburg, Ekkehard Sturm, Marcial Sebode, Ansgar W. Lohse, Philip Bufler. S3-Leitlinie „Seltene Lebererkrankungen (LeiSe LebEr) – Genetisch-cholestatische Lebererkrankungen von der Pädiatrie bis zum Erwachsenenalter“ der Deutschen Gesellschaft für Gastroenterologie, Verdauungs- und Stoffwechselkrankheiten (DGVS)Zeitschrift für Gastroenterologie 2026; 64(06) doi: 10.1055/a-2785-1072
16
Mukesh G. Harisinghani, Ranjodh Dhami, Aashna Karbhari, Riya Goyal, Soumyadeep Ghosh, Nabih Nakrour, Fatima Majeed, Nikita Consul, Nima Azimi, Monica Cheng, Robert Unger, Neha Udaykumar, Priyanka Naik, Danielle Barnett, Reece Goiffon, Nelson Gil, Madeleine Sertic. Abdominal and Pelvic Imaging Cases2024;  doi: 10.1007/978-3-031-68233-9_52
17
R. A. Gudkov, A. V. Dmitriev, O. A. Slobodyanyuk. Caroli syndrome in children: a brief review and clinical observationExperimental and Clinical Gastroenterology 2023; (10) doi: 10.31146/1682-8658-ecg-206-10-169-174
18
Teodor Cabel, Cristina Madalina Pascu, Catalin Stefan Ghenea, Bogdan Florin Dumbrava, Deniz Gunsahin, Andreea Andrunache, Livia-Marieta Negoita, Afrodita Panaitescu, Ecaterina Mihaela Rinja, Christopher Pavel, Oana-Mihaela Plotogea, Madalina Stan-Ilie, Vasile Sandru, Mariana Mihaila. Exceptional Liver Transplant Indications: Unveiling the Uncommon LandscapeDiagnostics 2024; 14(2) doi: 10.3390/diagnostics14020226
19
Muhammad Usman, Abdul Basit, Bilal Ahmad Buttar, Muhammad Aftab Ahmad, Laiba Murtaza. Recurrent Fever and Biliary Ectasia Leading to the Diagnosis of Caroli Syndrome: A Diagnostic ChallengeCureus 2026;  doi: 10.7759/cureus.111646
20
Mustafa Natout, Madiha M. Hijazi, Mutaz Kassas, Samir Mallat, Mohamad Haidar. Findings of cholangitis in a kidney transplant patient with Caroli disease on FDG PET/CT and MRIRadiology Case Reports 2023; 18(5) doi: 10.1016/j.radcr.2023.02.002
21
M. Ramírez Verdyguer, B. Mateos Muñoz, F.J. Manzano Gómez, J. López Cardona. Quistes hepáticosMedicine - Programa de Formación Médica Continuada Acreditado 2024; 14(9) doi: 10.1016/j.med.2024.05.004
22
Rachita Khot, Dhakshinamoorthy Ganeshan, Karthik M. Sundaram, Jena N. Depetris, Daniel R. Ludwig. Cystic lesions and their mimics involving the intrahepatic bile ducts and peribiliary space: diagnosis, complications, and managementAbdominal Radiology 2024; 50(7) doi: 10.1007/s00261-024-04742-6
23
A. Marichez, L. Chiche. Tumores biliares quísticos y no quísticos del hígadoEMC - Tratado de Medicina 2022; 26(4) doi: 10.1016/S1636-5410(22)47165-0
24
Luis F. Bonilla Larrama, Cesar U. Alas-Pineda, Anahi G. Pacheco, Victoria S. Díaz-Cerrato, Karla P. Molinero Leiva. Caroli disease incidentally discovered in a 23-years old male: A case reportRadiology Case Reports 2025; 20(1) doi: 10.1016/j.radcr.2024.09.080
25
Sabrina Groß, Michael Bitzer, Jörg Albert, Susanne Blödt, Judit Boda-Heggemann, Katrin Borucki, Thomas Brunner, Reiner Caspari, Frank Dombrowski, Matthias Evert, Markus Follmann, Paul Freudenberger, Cihan Gani, Jamila Gebert, Andreas Geier, Eleni Gkika, Martin Götz, Thomas Helmberger, Ralf-Thorsten Hoffmann, Peter Huppert, David Krug, Christian La Fougère, Hauke Lang, Thomas Langer, Philipp Lenz, Tom Lüdde, Andreas Mahnken, Silvio Nadalin, Hoa Huu Phuc Nguyen, Monika Nothacker, Johann Ockenga, Karl Oldhafer, Julia Ott, Philipp Paprottka, Philippe Pereira, Thorsten Persigehl, Ruben Plentz, Jürgen Pohl, Heinrich Recken, Peter Reimer, Jutta Riemer, Kristina Ringe, Elke Roeb, Jörn Rüssel, Barbara Schellhaas, Peter Schirmacher, Hans Jürgen Schlitt, Irene Schmid, Kerstin Schütte, Andreas Schuler, Daniel Seehofer, Marianne Sinn, Andreas Stengel, Nadine Steubesand, Christoph Stoll, Andrea Tannapfel, Anne Taubert, Jörg Trojan, Ingo van Thiel, Martin Utzig, Arndt Vogel, Thomas Vogl, Frank Wacker, Oliver Waidmann, Heiner Wedemeyer, Henning Wege, Gregor Wenzel, Dane Wildner, Marcus-Alexander Wörns, Peter Galle, Nisar Malek. S3-Leitlinie Diagnostik und Therapie biliärer Karzinome – LangversionZeitschrift für Gastroenterologie 2025; 63(02) doi: 10.1055/a-2460-6347
26
Dario Gambaccini, Giusi Desirè Sciumè, Luigi Ruggiero, Veronica Natali, Gherardo Tapete, Valeria Bolognesi, Emanuele Marciano. Suspected stenosis in Caroli syndrome: when cholangioscopy can be the game changerVideoGIE 2024; 9(6) doi: 10.1016/j.vgie.2024.03.004
27
Jesus Perez Orozo, Tatiana Paola Perez Garcia, Pedro Antonio Plaza Ricardo, Camila Gonzalez Fernandez de Castro, Andres David De leon Murillo. Manejo endoscópico de quiste hepático secundario a enfermedad de Caroli; una nueva era: a propósito de un caso Revista colombiana de Gastroenterología 2026; 41(2) doi: 10.22516/25007440.1350
28
Jie Zhao, Kang Yu, Yujuan Huang. Novel compound heterozygous PKHD1 mutations in a Chinese ARPKD pedigree and analysis of genotype-phenotype correlationsFrontiers in Medicine 2026; 13 doi: 10.3389/fmed.2026.1741795
29
Yongqin Ye, Vincent Chi Hang Lui, Paul Kwong Hang Tam. Pathogenesis of Choledochal Cyst: Insights from Genomics and TranscriptomicsGenes 2022; 13(6) doi: 10.3390/genes13061030
30
Cecilia Ferrari, Gian Mario D’Ambrosio, Belen Martın, Angel Garcia Romera, Vıctor Molina, Guido Griseri, Antonio Moral, Santiago Sánchez-Cabús. Intrahepatic Versus Extrahepatic Biliary Tree Cysts: Outcomes after Surgical Resection in a Multicentric StudyJournal of Laparoendoscopic & Advanced Surgical Techniques 2026; 36(2) doi: 10.1177/10926429251408365
31
Alexander Ney, Daniel C. Osei‐Bordom, Andres Garcia‐Sampedro, Pilar Acedo, Giuseppe K. Fusai, Martyn Stott, Phillip Hopley, Chandni Patel, Lucy Oldfield, William Greenhalf, Eithne Costello, Stephen P. Pereira. Gastrointestinal Oncology ‐ A Critical Multidisciplinary Team Approach 2e2024;  doi: 10.1002/9781119756422.ch17
32
Sabrina Groß, Michael Bitzer, Jörg Albert, Susanne Blödt, Judit Boda-Heggemann, Thomas Brunner, Reiner Caspari, Enrico De Toni, Frank Dombrowski, Matthias Evert, Markus Follmann, Paul Freudenberger, Cihan Gani, Andreas Geier, Eleni Gkika, Martin Götz, Thomas Helmberger, Ralf-Thorsten Hoffmann, Peter Huppert, David Krug, Christian La Fougère, Hauke Lang, Thomas Langer, Philipp Lenz, Tom Lüdde, Andreas Mahnken, Silvio Nadalin, Hoa Huu Phuc Nguyen, Monika Nothacker, Johann Ockenga, Karl Oldhafer, Philipp Paprottka, Philippe Pereira, Thorsten Persigehl, Ruben Plentz, Jürgen Pohl, Heinrich Recken, Peter Reimer, Jutta Riemer, Ulrike Ritterbusch, Elke Roeb, Jörn Rüssel, Barbara Schellhaas, Peter Schirmacher, Hans J. Schlitt, Irene Schmid, Andreas Schuler, Daniel Seehofer, Marianne Sinn, Andreas Stengel, Nadine Steubesand, Christoph Stoll, Andrea Tannapfel, Anne Taubert, Reina Tholen, Jörg Trojan, Ingo van Thiel, Arndt Vogel, Thomas Vogl, Frank Wacker, Oliver Waidmann, Heiner Wedemeyer, Henning Wege, Dane Wildner, Marcus-Alexander Wörns, Peter Galle, Nisar Malek. S3-Leitlinie „Diagnostik und Therapie biliärer Karzinome“ – Langversion 4.0Zeitschrift für Gastroenterologie 2024; 62(02) doi: 10.1055/a-2189-8567
33
Joost Drenth, Thijs Barten, Hermien Hartog, Frederik Nevens, Richard Taubert, Roser Torra Balcells, Valerie Vilgrain, Tobias Böttler. EASL Clinical Practice Guidelines on the management of cystic liver diseasesJournal of Hepatology 2022; 77(4) doi: 10.1016/j.jhep.2022.06.002
34
Mohammed H. Alsharif, Nagi.M Bakhit, Abdulaziz Alarifi, Elbagir M. Nassir, Abair A. Mahdi, Juman M. Almasaad, Abubaker.Y. Elamin, Khalid M. Taha. Hepatic multiple hyperintense cystic lesions: a rare caroli disease.THE NEW ARMENIAN MEDICAL JOURNAL 2023; (1, 17 (2023)) doi: 10.56936/18290825-2023.17.1-41
35
Han Meng, Ruiyu Xie, Chuanjie Yang. Ten-year progression of Caroli’s disease with portal hypertension despite endoscopic and pharmacological therapy: Implications for liver transplantation—A case reportSage Open Medical Case Reports 2026; 14 doi: 10.1177/2050313X261467162
36
M. Bitzer, S. Voesch, J. Albert, P. Bartenstein, W. Bechstein, S. Blödt, T. Brunner, F. Dombrowski, M. Evert, M. Follmann, C. La Fougère, P. Freudenberger, A. Geier, E. Gkika, M. Götz, E. Hammes, T. Helmberger, R. T. Hoffmann, W. P. Hofmann, P. Huppert, A. Kautz, G. Knötgen, J. Körber, D. Krug, F. Lammert, H. Lang, T. Langer, P. Lenz, A. Mahnken, A. Meining, O. Micke, S. Nadalin, H. P. Nguyen, J. Ockenga, K. Oldhafer, P. Paprottka, K. Paradies, P. Pereira, T. Persigehl, M. Plauth, R. Plentz, J. Pohl, J. Riemer, P. Reimer, J. Ringwald, U. Ritterbusch, E. Roeb, B. Schellhaas, P. Schirmacher, I. Schmid, A. Schuler, D. von Schweinitz, D. Seehofer, M. Sinn, A. Stein, A. Stengel, N. Steubesand, C. Stoll, A. Tannapfel, A. Taubert, J. Trojan, I. van Thiel, R. Tholen, A. Vogel, T. Vogl, H. Vorwerk, F. Wacker, O. Waidmann, H. Wedemeyer, H. Wege, D. Wildner, C. Wittekind, M. A. Wörns, P. Galle, N. Malek. S3-Leitlinie – Diagnostik und Therapie biliärer KarzinomeZeitschrift für Gastroenterologie 2022; 60(02) doi: 10.1055/a-1589-7854
37
Dr. Mohammed Elamin Elsirag, Dr. Adeel Afzal, Dr. Elfatih Elsiddig Hagelamin, Dr. Mahir Khiralla. Carolis Disease Presents as Acute Cholangitis and Recurrent Jaundice: A Case ReportInternational Journal of Advanced Medical Sciences and Technology 2026; 6(2) doi: 10.54105/ijamst.B3053.06020226
38
Piero Boraschi, Paola Scalise, Gaia Tarantini, Piero Colombatto, Francescamaria Donati. MR imaging features of multiple biliary hamartomas (Von Meyenburg Complex): A pictorial review and differential diagnosisJournal of Medical Imaging and Radiation Oncology 2021; 65(3) doi: 10.1111/1754-9485.13173
39
Nadia TOKARCHUK, Tetiana CHEKOTUN, Liudmyla STARYNETS. A clinical case of Caroli syndrome in a young childGazzetta Medica Italiana Archivio per le Scienze Mediche 2022; 181(5) doi: 10.23736/S0393-3660.21.04754-9
40
Mohammed H. Alsharif, Nagi M. Bakhit, Abdulaziz Alarifi, Elbagir M. Nassir, Abair A. Mahdi, Juman M. Almasaad, Abubaker Y. Elamin, Khalid M. Taha. Hepatic multiple hyperintense cystic lesions: a rare caroli diseaseTHE NEW ARMENIAN MEDICAL JOURNAL 2023; (1, 17 (2023)) doi: 10.56936/18290825-2023.17.41-45
41
Mohammad Saeid Rezaee-Zavareh, Ju Dong Yang. Biliary Tract Neoplasms2026;  doi: 10.1016/B978-0-443-29287-3.00016-7
42
Adem Ceri, Andreas Busse-Coté, Delphine Weil, Eric Delabrousse, Vincent Di Martino, Paul Calame. Non-infectious Hepatic Cystic Lesions: A Narrative ReviewCurrent Medical Imaging Formerly Current Medical Imaging Reviews 2025; 21 doi: 10.2174/0115734056358195250714053120
43
Fei Hou, Hao-Feng Xiong, Ying Liu, Shuang Zhao, Yi-Zhi Zhang, Qian Kang, Jing-Yi Liu, Lin Wei, Wei Qu, Zhi-Gui Zeng, Zhi-Jun Zhu, Li-Ying Sun. Clinical outcomes of liver transplantation in Caroli syndrome: a retrospective analysisOrphanet Journal of Rare Diseases 2025; 20(1) doi: 10.1186/s13023-025-03943-6
44
Seif Bugazia, Marie C. Hogan. Extrarenal Manifestations: Polycystic Liver Disease and Its ComplicationsAdvances in Kidney Disease and Health 2023; 30(5) doi: 10.1053/j.akdh.2023.10.004
45
Elaheh Karimzadeh‐Soureshjani, Farab Pourhasan, Pouria Ahmadi Simab, Sajjad Shojaei, Yasaman Mohammadian. A Rare Diagnosis of Caroli Syndrome in a Young PatientClinical Case Reports 2025; 13(6) doi: 10.1002/ccr3.70555
46
Jiawei Sun, Xiaoxiao Mi, Xiaoying Ye, Yiling ShenTu, Chun Liu, Dong Tang, WenJun Yang, Jie Yang, Xiaoping Ye, Xiaojie Ma, Junping Shi, Gongying Chen, Ling Gong. Biliary sepsis complication with congenital hepatic fibrosis: an unexpected outcomeBMC Infectious Diseases 2023; 23(1) doi: 10.1186/s12879-023-08681-3