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For: Hov JR, Boberg KM, Karlsen TH. Autoantibodies in primary sclerosing cholangitis. World J Gastroenterol 2008; 14(24): 3781-3791 [PMID: 18609700 DOI: 10.3748/wjg.14.3781]
URL: https://www.wjgnet.com/1007-9327/full/v14/i24/3781.htm
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Marco Vincenzo Lenti, Carlo Maria Rossi, Federica Melazzini, Matteo Gastaldi, Serena Bugatti, Mario Rotondi, Paola Ilaria Bianchi, Antonella Gentile, Luca Chiovato, Carlomaurizio Montecucco, Gino Roberto Corazza, Antonio Di Sabatino. Seronegative autoimmune diseases: A challenging diagnosis. Autoimmunity Reviews 2022; 21(9) doi: 10.1016/j.autrev.2022.103143
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D. Robert Dufour. Tietz Textbook of Clinical Chemistry and Molecular Diagnostics. 2012;  doi: 10.1016/B978-1-4160-6164-9.00050-0
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Evaggelia Liaskou, Gideon M. Hirschfield, M. Eric Gershwin. Mechanisms of tissue injury in autoimmune liver diseases. Seminars in Immunopathology 2014; 36(5) doi: 10.1007/s00281-014-0439-3
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David Tornai, Peter Laszlo Ven, Peter Laszlo Lakatos, Maria Papp. Serological biomarkers for management of primary sclerosing cholangitis. World Journal of Gastroenterology 2022; 28(21): 2291-2301 doi: 10.3748/wjg.v28.i21.2291
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José Franco. Liver Disorders. 2017;  doi: 10.1007/978-3-319-30103-7_17
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Pan Luo, Lin Liu, Weikun Hou, Ke Xu, Peng Xu, Nadeem Sheikh. Gene Set Enrichment Analysis Detected Immune Cell‐Related Pathways Associated with Primary Sclerosing Cholangitis. BioMed Research International 2022; 2022(1) doi: 10.1155/2022/2371347
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S3-Leitlinie „Seltene Lebererkrankungen (LeiSe LebEr) – Autoimmune Lebererkrankungen von der Pädiatrie bis zum Erwachsenenalter“ der Deutschen Gesellschaft für Gastroenterologie, Verdauungs- und Stoffwechselkrankheiten (DGVS). Zeitschrift für Gastroenterologie 2025; 63(06) doi: 10.1055/a-2558-5204
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Matteo Bramuzzo, Stefano Martelossi, Giuliano Torre, Sabrina Cardile, Serena Arrigo, Silvia Vignola, Federica Ferrari, Giovanna Zuin, Maria Teresa Illiceto, Marco Gasparetto, Salvatore Pellegrino, Claudio Romano, Giuseppe Maggiore, Marcella Montico, Marina Aloi. Clinical Features and Risk Factors of Autoimmune Liver Involvement in Pediatric Inflammatory Bowel Disease. Journal of Pediatric Gastroenterology and Nutrition 2016; 63(2) doi: 10.1097/MPG.0000000000001078
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Dermot Gleeson, Rosemary Bornand, Ann Brownlee, Harpreet Dhaliwal, Jessica K Dyson, Janeane Hails, Paul Henderson, Deirdre Kelly, George F Mells, Rosa Miquel, Ye H Oo, Anthea Sutton, Andrew Yeoman, Michael A Heneghan. British Society of Gastroenterology guidelines for diagnosis and management of autoimmune hepatitis. Gut 2025; 74(9) doi: 10.1136/gutjnl-2024-333171
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Vincenzo Ronca, Maria-Carlota Londoño. Primary sclerosing cholangitis pathogenesis revisited: EBV-idence of immune dysregulation. JHEP Reports 2026; 8(3) doi: 10.1016/j.jhepr.2025.101665
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Alpha Boubacar Conte, Fatoumata Coulibaly, Sofia Jayi, Fatima Zohra Fdili Alaoui, Hikmat Chaara, Moulay Abdelilah Melhouf. Primary sclerosing cholangitis revealed by pregnancy. Obstetrics & Gynecology International Journal 2023; 14(2) doi: 10.15406/ogij.2023.14.00695
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Ida Schregel, Silja Steinmann, Christoph Schramm. Autoimmune Lebererkrankungen – ein Update (Teil 2). Gastroenterologie up2date 2022; 18(03) doi: 10.1055/a-1922-9264
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Kirsten Muri Boberg, Roger W. Chapman, Gideon M. Hirschfield, Ansgar W. Lohse, Michael P. Manns, Erik Schrumpf. Overlap syndromes: The International Autoimmune Hepatitis Group (IAIHG) position statement on a controversial issue. Journal of Hepatology 2011; 54(2) doi: 10.1016/j.jhep.2010.09.002
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A. Schreiber, B. Rudolph, A. Kahl, R. Kettritz. Akutes Nierenversagen bei einem lebertransplantierten Patienten. Der Nephrologe 2015; 10(5) doi: 10.1007/s11560-014-0932-7
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Brian K. Chung, Gideon M. Hirschfield. Immunogenetics in primary sclerosing cholangitis. Current Opinion in Gastroenterology 2017; 33(2) doi: 10.1097/MOG.0000000000000336
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Tom H. Karlsen, Trine Folseraas, Douglas Thorburn, Mette Vesterhus. Primary sclerosing cholangitis – a comprehensive review. Journal of Hepatology 2017; 67(6) doi: 10.1016/j.jhep.2017.07.022
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Dominik Roth, Miriam M Düll, Ludwig J Horst, Aylin Lindemann, Xenia Malzer, Kristina Koop, Sebastian Zundler, Marcel Vetter, André Jefremow, Raja Atreya, Carol Geppert, Sören Weidemann, Maximilian J Waldner, Peter Dietrich, Claudia Günther, Luis E Munoz, Martin Herrmann, Alexander Scheffold, Markus F Neurath, Jürgen Siebler, Christoph Schramm, Andreas E Kremer, Moritz Leppkes. Integrin αVβ6: Autoantigen and Driver of Epithelial Remodeling in Colon and Bile Ducts in Primary Sclerosing Cholangitis and Inflammatory Bowel Disease. Journal of Crohn's and Colitis 2025; 19(2) doi: 10.1093/ecco-jcc/jjae131
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Byoung Uk Park, Zongming Eric Chen. Practical Liver Pathology. Practical Anatomic Pathology 2025;  doi: 10.1007/978-3-031-97506-6_10
20
Shou-Pei Liu, Zhen-Hua Bian, Zhi-Bin Zhao, Jinjun Wang, Weici Zhang, Patrick S.C. Leung, Liang Li, Zhe-Xiong Lian. Animal Models of Autoimmune Liver Diseases: a Comprehensive Review. Clinical Reviews in Allergy & Immunology 2020; 58(2) doi: 10.1007/s12016-020-08778-6
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Elisabeth M.G. de Vries, Ulrich Beuers, Cyriel Y. Ponsioen. Biomarkers for disease progression of primary sclerosing cholangitis. Current Opinion in Gastroenterology 2015; 31(3) doi: 10.1097/MOG.0000000000000163
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Hiroyuki Isayama, Susumu Tazuma, Norihiro Kokudo, Atsushi Tanaka, Toshio Tsuyuguchi, Takahiro Nakazawa, Kenji Notohara, Suguru Mizuno, Nobuhisa Akamatsu, Masahiro Serikawa, Itaru Naitoh, Yoshiki Hirooka, Toshifumi Wakai, Takao Itoi, Tomoki Ebata, Shinji Okaniwa, Terumi Kamisawa, Hiroki Kawashima, Atsushi Kanno, Keiichi Kubota, Masami Tabata, Michiaki Unno, Hajime Takikawa. Clinical guidelines for primary sclerosing cholangitis 2017. Journal of Gastroenterology 2018; 53(9) doi: 10.1007/s00535-018-1484-9
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Kayani Kayani, Amber G Bozward, Scott P Davies, Rebecca Jeyaraj, Ayma Asif, Ye H Oo. Encyclopedia of Immunobiology. 2026;  doi: 10.1016/B978-0-12-824465-4.00173-3
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Laura Räisänen, Christopher Burgess, Fariha Balouch, Peter Lewindon. Proximally dominant inflammation at colonoscopy predicts pan-colonic histological remission following oral vancomycin therapy in pediatric ulcerative colitis. Digestive and Liver Disease 2026; 58(8) doi: 10.1016/j.dld.2026.06.001
25
Marcial Sebode, Heike Bantel, Ulrich Baumann, Philip Bufler, Münevver Demir, Leona Dold, Verena Keitel-Anselmino, Reinhild Klein, Andreas E. Kremer, Petra L. Jansen, Michael Melter, Peter Schirmacher, Christoph Schramm, Martina Sterneck, Christian P. Strassburg, Christina Weiler-Normann, Ansgar W. Lohse. Update der S3-Leitlinie „Seltene Lebererkrankungen (LeiSe LebEr) – Autoimmune Lebererkrankungen von der Pädiatrie bis zum Erwachsenenalter“ der Deutschen Gesellschaft für Gastroenterologie, Verdauungs- und Stoffwechselkrankheiten (DGVS) – Living guideline. Zeitschrift für Gastroenterologie 2026; 64(05) doi: 10.1055/a-2769-2475
26
Takuma Misawa, Jeffrey A. SoRelle, Jin Huk Choi, Tao Yue, Kuan-wen Wang, William McAlpine, Jianhui Wang, Aijie Liu, Koichi Tabeta, Emre E. Turer, Bret Evers, Evan Nair-Gill, Subhajit Poddar, Lijing Su, Feiya Ou, Liyang Yu, Jamie Russell, Sara Ludwig, Xiaoming Zhan, Sara Hildebrand, Xiaohong Li, Miao Tang, Anne R. Murray, Eva Marie Y. Moresco, Bruce Beutler. Mutual inhibition between Prkd2 and Bcl6 controls T follicular helper cell differentiation. Science Immunology 2020; 5(43) doi: 10.1126/sciimmunol.aaz0085
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Silja Steinmann, Ida Schregel, Christoph Schramm. Autoimmune Lebererkrankungen – ein Update (Teil 1). Gastroenterologie up2date 2022; 18(03) doi: 10.1055/a-1364-8489
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James P. Stevens, Nitika A. Gupta. Recent Insights into Pediatric Primary Sclerosing Cholangitis. Clinics in Liver Disease 2022; 26(3) doi: 10.1016/j.cld.2022.03.009
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Vitantonio GUGLIELMI, Pietro GIORGIO, Vito GUERRA, Anna SONNANTE, Massimo TUTINO, Rossella DONGHIA, Antonio PISANI. Prognostic value of perinuclear antineutrophil cytoplasmic antibodies in subjects with primary sclerosing cholangitis. Minerva Medica 2022; 113(3) doi: 10.23736/S0026-4806.20.06604-5
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T. Liwinski, C. Schramm. Primär sklerosierende Cholangitis. Der Internist 2018; 59(6) doi: 10.1007/s00108-018-0428-z
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Maria C. SORRENTINO, Teresa CARBONE, Luigi CINQUANTA, Maria G. ALESSIO, Maria INFANTINO, Gaia DELEONARDI, Maria T. TREVISAN, Brunetta PORCELLI, Lucia TERZUOLI, Stefan PLATZGUMMER, Ignazio BRUSCA, Antonio ANTICO, Marilina TAMPOIA, Giampaola PESCE, Danilo VILLALTA, Nicola BIZZARO. Linee guida SIPMeL per la determinazione degli autoanticorpi nella diagnosi delle malattie autoimmuni del fegato. La Rivista Italiana della Medicina di Laboratorio 2024; 20(1) doi: 10.23736/S1825-859X.24.00226-3
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Stefano Fiorucci, Silvia Marchianò, Ginevra Urbani, Cristina Di Giorgio, Eleonora Distrutti, Angela Zampella, Michele Biagioli. Immunology of bile acids regulated receptors. Progress in Lipid Research 2024; 95 doi: 10.1016/j.plipres.2024.101291
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Yash R Shah, Natalia Nombera-Aznaran, David Guevara-Lazo, Ernesto Calderon-Martinez, Angad Tiwari, SriLakshmiDevi Kanumilli, Purva Shah, Bhanu Siva Mohan Pinnam, Hassam Ali, Dushyant Singh Dahiya. Liver transplant in primary sclerosing cholangitis: Current trends and future directions. World Journal of Hepatology 2023; 15(8): 939-953 doi: 10.4254/wjh.v15.i8.939
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Rosebella A. Iseme, Mark McEvoy, Brian Kelly, Linda Agnew, Frederick R. Walker, Michael Boyle, John Attia. A Cross-Sectional Study of the Association between Autoantibodies and Qualitative Ultrasound Index of Bone in an Elderly Sample without Clinical Autoimmune Disease. Journal of Immunology Research 2018; 2018 doi: 10.1155/2018/9407971
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Vasiliy Ivanovich Reshetnyak, Alexandra Andreevna Reshetnyak, Igor Veniaminovich Maev. Peribiliary and colonic crypt glands in primary sclerosing cholangitis and inflammatory bowel disease pathogenesis: New research perspectives. World Journal of Hepatology 2026; 18(8): 123377 doi: 10.4254/wjh.123377
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Caterina Maria Gambino, Luisa Agnello, Vincenza Calvaruso, Rosaria Vincenza Giglio, Luigi Capodicasa, Concetta Scazzone, Giuseppina Candore, Fabio Del Ben, Vito Di Marco, Marcello Ciaccio. Prevalence and heterogeneity of antinuclear antibody patterns in adult Italian patients with autoimmune liver diseases: Our experience. Clinica Chimica Acta 2025; 566 doi: 10.1016/j.cca.2024.120037
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Beate Preuß, Amelie Frank, Birgit Terjung, Ulrich Spengler, Christoph Berg, Reinhild Klein. Autoantibodies to beta tubulin in autoimmune liver diseases—Relation to pANCA and clinical relevance. Clinical and Experimental Immunology 2024; 216(2) doi: 10.1093/cei/uxad114
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Johannes R. Hov, Tom H. Karlsen. The microbiota and the gut–liver axis in primary sclerosing cholangitis. Nature Reviews Gastroenterology & Hepatology 2023; 20(3) doi: 10.1038/s41575-022-00690-y
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Hyun Jin Cha, Jimin Hwang, Lucy Eunju Lee, Younhee Park, Jason Jungsik Song, Gianfranco D. Alpini. The significance of cytoplasmic antinuclear antibody patterns in autoimmune liver disease. PLOS ONE 2021; 16(1) doi: 10.1371/journal.pone.0244950
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Benedetta Terziroli Beretta-Piccoli, Giorgina Mieli-Vergani, Diego Vergani. The clinical usage and definition of autoantibodies in immune-mediated liver disease: A comprehensive overview. Journal of Autoimmunity 2018; 95 doi: 10.1016/j.jaut.2018.10.004
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Mohammed Rifat Shaik, Hee Jae Jung, Nishat Anjum Shaik, Jamal Mikdashi. Diseases of the Gallbladder and the Biliary Tree in Systemic Lupus Erythematosus: Review of Clinical Presentation, Diagnosis and Management. Indian Journal of Rheumatology 2025; 20(2) doi: 10.1177/09733698241300754
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Sigrid Næss, Alexey Shiryaev, Johannes R. Hov, Andre Franke, Tom H. Karlsen. Genetics in primary sclerosing cholangitis. Clinics and Research in Hepatology and Gastroenterology 2012; 36(4) doi: 10.1016/j.clinre.2012.02.003
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Dong Xi, Henry Lin, Amit A. Shah. Overview of autoimmune liver disease: Prevalence, risk factors, and role of autoantibodies. Clinical Liver Disease 2022; 20(4) doi: 10.1002/cld.1227
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A. V. Nikitin, G. V. Volynets. Sclerosing cholangitis and inflammatory bowel disease: which comes first?. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics) 2021; 66(1) doi: 10.21508/1027-4065-2021-66-1-39-46
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Kai Markus Schneider, Martin Kummen, Palak J. Trivedi, Johannes R. Hov. Role of microbiome in autoimmune liver diseases. Hepatology 2024; 80(4) doi: 10.1097/HEP.0000000000000506
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Brian K. Chung, Eva Kristine Klemsdal Henriksen, Kristin Kaasen Jørgensen, Tom H. Karlsen, Gideon M. Hirschfield, Evaggelia Liaskou. Gut and Liver B Cells of Common Clonal Origin in Primary Sclerosing Cholangitis–Inflammatory Bowel Disease. Hepatology Communications 2018; 2(8) doi: 10.1002/hep4.1200
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Hyeok Choi, Yong-Beom Park, Jaewoo Song, Sang-Won Lee. Unclassifiable repeated antineutrophil cytoplasmic antibody (ANCA) positivity in diseases other than ANCA-associated vasculitis. Zeitschrift für Rheumatologie 2022; 81(8) doi: 10.1007/s00393-021-00998-1
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Senka Dobric, Dragan Popovic, Milos Nikolic, Sladjana Andrejevic, Milan Spuran, Branka Bonaci-Nikolic. Anti-neutrophil cytoplasmic antibodies (ANCA) specific for one or several antigens: useful markers for subtypes of ulcerative colitis and associated primary sclerosing cholangitis. Clinical Chemistry and Laboratory Medicine 2012; 50(3) doi: 10.1515/cclm.2011.797
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